Hereditary and congenital bronchiectasis

Hereditary and congenital are actually two manifestations of cause and effect. Of course, among all the causes of bronchiectasis, such as infection, cilia abnormality, heredity, immune deficiency, foreign body inhalation, the proportion of hereditary disease is very small, but it is very important only from the in-depth analysis of hereditary and congenital bronchial asthma.

Bronchiectasis Marfan syndrome

Congenital bronchiectasis is due to congenital bronchial defects, including hereditary cystic fibrosis, α 1 antitrypsin deficiency, yellow nail syndrome, pulmonary sequestration, etc., and may also be congenital mucociliary clearance dysfunction, such as primary ciliary immobility syndrome. It may also be congenital and genetic constitution, the development of hoof tissue is weak, or there is Marfan syndrome in heredity.

Then cut from the Malaysia syndrome: the performance of the body has slender limbs, arms flat fingers longer than the length of the body, spider fingers or toes. When drooping, the upper body is longer than the lower body. There are also long head deformity, narrow face, high palatal arch, low ear position, low fat, underdeveloped muscle, chest, abdomen and arm skin wrinkles. Show powerless physique because of low muscle tension, or have funnel chest, chicken chest, kyphosis or scoliosis, spina bifida and so on.

Congenital cataract caused by bronchiectasis

In the eye and cardiovascular aspects, people with Marfan syndrome are also different, there may be lens dislocation or subluxation, high myopia, cataract, retinal detachment, iris tremor and so on, this phenomenon is more male than female. On the cardiovascular side, 80% of congenital bronchiectasis has congenital cardiovascular malformations, including progressive dilatation of the main arteries and aortic insufficiency.